Fifty-five patients with disorders of intestinal rotation (DIR) are reviewed. Dir can occur at any age. Twenty-nine adults and twenty-six children were treated in this group. The clinical manifestation is mainly that of intestinal obstruction, with an incidence of 85%. In this group, 11 patients were complicated with other congenital malformation, and the incidence was 20%. It is difficult to diagnose DIR from the clinical manifestation, but the definite diagnosis can be made by roentgenography in most patients. Surgery can treat the intestinal obstruction and associated malformation synchronously. The results of treatment were satisfactory.